Projects per year
Personal profile
Campus career
附属病院 特命講師 2018/06/01-2019/09/30
附属病院 特命講師 2019/10/01-
医学系 特命講師 2019/10/01-
Research interests
2) 心筋緻密化障害の臨床像と心臓再同期療法を含む治療法の研究
3) Danon病など二次性心筋症の臨床遺伝学的研究
4) 川崎病冠動脈障害進展機序に関する研究(EMP, CyA, micro RNA, テネイシンなど)
5) Fontan術後患者における肝線維化など長期予後に関する研究療
Research Fields, Keywords
- cardiomyopathy
- Kawasaki disease
Field of expertise (Grants-in-aid for Scientific Research classification)
- Pediatrics
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- 1 Similar Profiles
Collaborations and top research areas from the last five years
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原因不明の心臓突然死の診断,病態解明に向けた網羅的剖検研究
Hata, Y. (Principal Investigator), Nishida, N. (Co-Investigator(Kenkyū-buntansha)), 森宙史 (Co-Investigator(Kenkyū-buntansha)), Ichimata, S. (Co-Investigator(Kenkyū-buntansha)) & Hirono, K. (Co-Investigator(Kenkyū-buntansha))
Japan Society for the Promotion of Science
2025/04/01 → 2028/03/31
Project: Research Project
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血管内皮障害と脈管増生因子に基づくフォンタン術後リンパ系合併症の病態解明
Ibuki, K. (Principal Investigator), Taguchi, M. (Co-Investigator(Kenkyū-buntansha)), Nakaoka, H. (Co-Investigator(Kenkyū-buntansha)), Ozawa, S. (Co-Investigator(Kenkyū-buntansha)), Hirono, K. (Co-Investigator(Kenkyū-buntansha)) & Imamura, T. (Co-Investigator(Kenkyū-buntansha))
Japan Society for the Promotion of Science
2025/04/01 → 2028/03/31
Project: Research Project
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フォンタン術後のタンパク漏出性胃腸症の早期発見と治療に向けた基盤の構築
Ibuki, K. (Principal Investigator), Nakaoka, H. (Co-Investigator(Kenkyū-buntansha)), Ozawa, S. (Co-Investigator(Kenkyū-buntansha)), Hirono, K. (Co-Investigator(Kenkyū-buntansha)) & Imamura, T. (Co-Investigator(Kenkyū-buntansha))
Japan Society for the Promotion of Science
2022/04/01 → 2025/03/31
Project: Research Project
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MYH7の多様性に着目した心筋緻密化障害の病態の解明
Hirono, K. (Principal Investigator), Nakagawa, T. (Co-Investigator(Kenkyū-buntansha)), Hasegawa, H. (Co-Investigator(Kenkyū-buntansha)), Nishida, N. (Co-Investigator(Kenkyū-buntansha)), Ibuki, K. (Co-Investigator(Kenkyū-buntansha)), Hata, Y. (Co-Investigator(Kenkyū-buntansha)) & Ozawa, S. (Co-Investigator(Kenkyū-buntansha))
Japan Society for the Promotion of Science
2022/04/01 → 2025/03/31
Project: Research Project
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Long-term follow-up of patients with catecholaminergic polymorphic ventricular tachycardia related to a novel CALM2 variant
Ohno, S., Kato, K., Fukuyama, M., Hirono, K., Nishida, K. & Horie, M., 2026/01, In: Journal of Cardiology Cases. 33, 1, p. 6-8 3 p.Research output: Contribution to journal › Article › peer-review
Open Access -
Evaluation of multiple ventricular septal defects using three-dimensional reconstruction models
Yoshimura, N., Aoki, M., Toritsuka, D., Motono, S., Nagura, S., Doi, T., Fukahara, K., Nakaoka, H., Ibuki, K., Ozawa, S. & Hirono, K., 2025/05/01, In: European Journal of Cardio-thoracic Surgery. 67, 5, ezaf080.Research output: Contribution to journal › Article › peer-review
1 Scopus citations -
Initial Experience of Noninvasive Quantification of Pulmonary Congestion Utilizing the Remote Dielectric Sensing System in Pediatric Patients with Heart Failure
Okabe, M., Imamura, T., Nishiyama, M., Nakaoka, H., Ibuki, K., Ozawa, S. & Hirono, K., 2025/02, In: Journal of Clinical Medicine. 14, 4, 1292.Research output: Contribution to journal › Article › peer-review
Open Access -
Left Ventricular Noncompaction Cardiomyopathy in Children: A Focus on Genetic and Molecular Mechanisms
Lehman, M. B., Orgil, B. O., Guerrier, K., Hirono, K., Batsaikhan, E., Saito, K., Collyer, J. W., Towbin, J. A. & Purevjav, E., 2025/08, In: Reviews in Cardiovascular Medicine. 26, 8, 39044.Research output: Contribution to journal › Review article › peer-review
Open Access2 Scopus citations -
Metabolic remodeling and cardiac dysfunction in left ventricular noncompaction: Insights from the MYH7 Q315R model
Takarada, S., Hata, Y., Yaku, K., Izumi, H., Fujii, K., Omura, M., Takasaki, I., Tsuboi, K., Okabe, M., Miyao, N., Nakaoka, H., Ibuki, K., Ozawa, S., Nakagawa, T., Hasegawa, H., Ichimata, S., Nishida, N., Mori, H., Yanagibashi, Y. & Takao, K. & 2 others, , 2025/11, In: PLoS ONE. 20, 11 November, e0336131.Research output: Contribution to journal › Article › peer-review
Open Access
Datasets
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Clinicopathological features of clinically undiagnosed sporadic transthyretin cardiac amyloidosis: a forensic autopsy-based series
Ichimata, S. (Contributor), Hata, Y. (Creator), Hirono, K. (Creator), Yamaguchi, Y. (Creator) & Nishida, N. (Creator), Taylor & Francis, 2021
DOI: 10.6084/m9.figshare.13737588, https://tandf.figshare.com/articles/dataset/Clinicopathological_features_of_clinically_undiagnosed_sporadic_transthyretin_cardiac_amyloidosis_a_forensic_autopsy-based_series/13737588
Dataset
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Clinicopathological features of clinically undiagnosed sporadic transthyretin cardiac amyloidosis: a forensic autopsy-based series
Ichimata, S. (Contributor), Hata, Y. (Creator), Hirono, K. (Creator), Yamaguchi, Y. (Creator) & Nishida, N. (Creator), Taylor & Francis, 2021
DOI: 10.6084/m9.figshare.13737588.v1, https://tandf.figshare.com/articles/dataset/Clinicopathological_features_of_clinically_undiagnosed_sporadic_transthyretin_cardiac_amyloidosis_a_forensic_autopsy-based_series/13737588/1
Dataset
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Reversible left ventricular noncompaction caused by hypertensive hydrocephalus: a pediatric case report
Kato, R. (Creator), Taneichi, H. (Creator), Takarada, S. (Creator), Okabe, M. (Creator), Miyao, N. (Creator), Nakaoka, H. (Creator), Ibuki, K. (Contributor), Ozawa, S. (Creator), Adachi, Y. (Creator), Yoshimura, N. (Creator), Saito, K. (Creator), Ichida, F. (Contributor) & Hirono, K. (Creator), figshare, 2021
DOI: 10.6084/m9.figshare.c.5407141, https://springernature.figshare.com/collections/Reversible_left_ventricular_noncompaction_caused_by_hypertensive_hydrocephalus_a_pediatric_case_report/5407141
Dataset
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Reversible left ventricular noncompaction caused by hypertensive hydrocephalus: a pediatric case report
Kato, R. (Creator), Taneichi, H. (Creator), Takarada, S. (Creator), Okabe, M. (Creator), Miyao, N. (Creator), Nakaoka, H. (Creator), Ibuki, K. (Contributor), Ozawa, S. (Creator), Adachi, Y. (Creator), Yoshimura, N. (Creator), Saito, K. (Creator), Ichida, F. (Contributor) & Hirono, K. (Creator), figshare, 2021
DOI: 10.6084/m9.figshare.c.5407141.v1, https://springernature.figshare.com/collections/Reversible_left_ventricular_noncompaction_caused_by_hypertensive_hydrocephalus_a_pediatric_case_report/5407141/1
Dataset
Courses
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小児臨床医学
Miya, K., Takasaki, A., Nomura, K., Hirono, K., Tanaka, T., Ibuki, K., Ozawa, S., Taneichi, H., Tamura, K. & Imai, C. 2024/10/01 → 2025/03/31
Course
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循環器系
Sasahara, M., Yoshimura, N., Fukahara, K., Joho, S., Kataoka, N., Sobajima, M., Fukuda, N., Hirono, K., Kinugawa, K., Koike, T., Imamura, T., Ueno, H., Ushijima, R., Nakamura, M. & Yamashita, S. 2024/04/01 → 2025/03/31
Course
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成長と発達
Miya, K., Nomura, K., Hirano, K., Hirono, K., Tanaka, T., Yoshida, T., Ozawa, S., Taneichi, H., Tamura, K., Imai, C. & Hiraiwa, A. 2024/04/01 → 2024/09/30
Course
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小児科
Takasaki, A., Nomura, K., Hirono, K., Tanaka, T., Yoshida, T., Ibuki, K., Ozawa, S., Taneichi, H., Tamura, K. & Imai, C. 2024/04/01 → 2025/03/31
Course
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医用工学
Noguchi, K., Shakunaga, K., Hirono, K., Kitamura, H., Fujisaka, M., Saitoh, J.-I., Takakura, H. & Nakamura, M. 2023/10/01 → 2024/03/31
Course